Case Report: Androgen-secreting pediatric adrenocortical tumor of uncertain malignant potential presenting with virilization in a 19-month-old girl

    July 2026 in “ Frontiers in Endocrinology
    Yirong Wang, Bo Sun, X T Lu, Tongmin Li, Mei Han, Hongbin Hou
    A 19-month-old girl presented with virilization symptoms due to an androgen-secreting adrenocortical tumor (ACT) of uncertain malignant potential. The tumor was surgically removed, and postoperative androgen levels significantly decreased, maintaining biochemical remission at 4 and 8 months. The case highlights the importance of adrenal-focused assessment in young girls with rapid virilization. Long-term surveillance is recommended, including endocrine assessment, pubertal monitoring, and genetic counseling, as early remission does not rule out recurrence or secondary central precocious puberty.
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