Atrichia Congenita With Papular Lesions: A Rare Cause of Pediatric Alopecia

Congenital atrichia with papules is a rare genetic disorder where hair follicles are replaced by keratinous cysts, leading to hair loss soon after birth and the development of papular lesions. It is important to distinguish this condition from other causes of congenital atrichia, like vitamin D-dependent rickets, alopecia universalis, and ectodermal dysplasia, to prevent unnecessary treatments and to inform parents about its benign yet irreversible nature.